Table 1

Rare tumour types

Tier	System	Tumour types	ICD code
	1. Head and neck tumour
1		Epithelial tumours of the eye and adnexa	C69
2		Epithelial tumours of the middle ear	C69
3		Squamous carcinoma	C69
3		Basal cell carcinoma	C69
2		Variants of adenocarcinoma of the eye and adnexa	C69
3		Adenocarcinoma, NOS	C69
3		Adenoid cystic carcinoma	C69
3		Mucoepidermoid carcinoma	C69
1		Epithelial tumours of the nasal cavity	CD30
1		Epithelial tumours of the sinuses	CD31
2		Lymphoepithelial carcinoma of the nasal cavity and sinuses	C30, C31
2		Undifferentiated carcinoma of the nasal cavity and sinuses	C30, C31
2		Intestinal type adenocarcinoma of the nasal cavity and sinuses	C30, C31
1		Epithelial tumours of the middle ear	C30
2		Variants of squamous cell carcinoma of the middle ear	C30
3		Squamous carcinoma	C30
2		Variants of adenocarcinoma of the middle ear	C30
3		Adenocarcinoma, NOS	C30
3		Adenoid cystic carcinoma	C30
1		Odontogenic malignant tumours	C03
2		Odontogenic malignant tumours	C03
3		Clear Cell Odontogenic Carcinoma	C03
1		Eepithelial tumours of major salivary glands and salivary-gland-type tumours	C00-C14, C30, C31, C32
2		Malignant tumour of the parotid gland	C07
3		Squamous carcinoma	C7, C8
3		Large cell carcinoma	C7, C8
3		Lymphoepithelial carcinoma	C7, C8
3		Carcinosarcoma, NOS	C7, C8
3		Adenocarcinoma, NOS	C7, C8
3		Clear cell adenocarcinoma, NOS	C7, C8
3		Mucinous adenocarcinoma	C7, C8
3		Ductal carcinoma	C7, C8
3		Oxyphilic adenocarcinoma	C7, C8
3		Papillary cystadenocarcinoma, NOS	C7, C8
3		Adenoid cystic carcinoma	C7, C8
3		Mucoepidermoid carcinoma	C7, C8
3		Acinar cell adenocarcinoma	C7, C8
3		Malignant myoepithelioma	C7, C8
3		Carcinoma in pleomorphic adenoma	C7, C8
3		Mixed tumour, malignant	C7, C8
3		Polymorphous low-grade adenocarcinoma	C7, C8
3		Basal cell adenocarcinoma	C7, C8
3		Epithelial-myoepithelial carcinoma	C7, C8
3		Sebaceous adenocarcinoma	C7, C8
3		Cystadenocarcinoma, NOS	C7, C8
3		Low-grade cribriform cystadenocarcinoma	C7, C8
3		Mammary Analogue Secretory Carcinoma of Salivary Gland Origin	C7, C8
3		Salivary Adenocarcinoma	C7, C8
2		Epithelial tumours of major salivary glands	C08
3		Mucoepidermoid carcinoma	C00–C06, C09–C14, C30, C31, C32
3		Adenocarcinoma, NOS	C00–C06, C09–C14, C30, C31, C32
3		Adenoid cystic carcinoma	C00–C06, C09–C14, C30, C31, C32
3		Acinar cell adenocarcinoma	C00–C06, C09–C14, C30, C31, C32
3		Ductal carcinoma	C00–C06, C09–C14, C30, C31, C32
3		Mucinous adenocarcinoma	C00–C06, C09–C14, C30, C31, C32
3		Basal cell adenocarcinoma	C00–C06, C09–C14, C30, C31, C32
3		Clear cell adenocarcinoma, NOS	C00–C06, C09–C14, C30, C31, C32
3		Epithelial-myoepithelial carcinoma	C00–C06, C09–C14, C30, C31, C32
3		Polymorphous low-grade adenocarcinoma	C00–C06, C09–C14, C30, C31, C32
3		Carcinoma in pleomorphic adenoma	C00–C06, C09–C14, C30, C31, C32
3		Malignant myoepithelioma	C00–C06, C09–C14, C30, C31, C32
3		Cystadenocarcinoma, NOS	C00–C06, C09–C14, C30, C31, C32
3		Oncocytic carcinoma	C00–C06, C09–C14, C30, C31, C32
3		Papillary cystadenocarcinoma, NOS	C00–C06, C09–C14, C30, C31, C32
2		Medullary thyroid carcinoma
	2. Digestive system tumours
2		Salivary-gland-type tumours of the oesophagus	C15
3		Mucoepidermoid carcinoma	C15
3		Adenoid cystic carcinoma	C15
2		Undifferentiated carcinoma of the oesophagus	C15
2		Salivary-gland-type tumours of the stomach	C16
3		Mucoepidermoid carcinoma	C16
3		Adenoid cystic carcinoma	C16
1		Epithelial tumours of the small intenstine	C17
2		Variants of adenocarcinoma of the small intestine	C17
3		Adenocarcinoma, NOS	C17
3		Mucinous adenocarcinoma	C17
3		Signet ring cell carcinoma	C17
3		Adenosquamous carcinoma	C17
3		Medullary carcinoma, NOS	C17
3		Undifferentiated carcinoma	C17
2		Variants of squamous cell carcinoma of the small intestine	C17
3		Squamous carcinoma	C17
3		Undifferentiated carcinoma	C20
3		Medullary carcinoma, NOS	C20
2		Serous cystadenocarcinoma of the pancreas	C25
2		Carcinoma with osteoclast-like giant cells of the pancreas	C25
2		Liver Angiosarcoma	C22
2		Malignant Rhabdoid Tumour of the Liver	C22
2		Undifferentiated Embryonal Sarcoma of the Liver	C22
2		Malignant Nonepithelial Tumour of the Liver	C22
1		Epithelial tumours of the gallbladder	C23
1		Epithelial tumours of the extrahepatic biliary tract (EBT) and unspecified regions	C24
2		Small Cell Gallbladder Carcinoma	C23
2		Variants of adenocarcinoma of the gallbladder	C23
3		Cholangiocarcinoma	C23
3		Papillary adenocarcinoma, NOS	C23
3		Adenocarcinoma intestinal type	C23
3		Mucinous adenocarcinoma	C23
3		Clear cell adenocarcinoma, NOS	C23
3		Signet ring cell carcinoma	C23
3		Adenosquamous carcinoma	C23
3		Undifferentiated carcinoma	C23
3		Bile duct cystadenocarcinoma	C23
2		Cholangiocarcinoma of IBT	C22
2		Variants of adenocarcinoma of EBT	C24
3		Cholangiocarcinoma	C24
3		Papillary adenocarcinoma, NOS	C24
3		Adenocarcinoma intestinal type	C24
3		Mucinous adenocarcinoma	C24
3		Clear cell adenocarcinoma, NOS	C24
3		Signet ring cell carcinoma	C24
3		Adenosquamous carcinoma	C24
3		Undifferentiated carcinoma	C24
3		Bile duct cystadenocarcinoma	C24
2		Squamous cell carcinoma of gallbladder and EBT	C23, C24
	3. Respiratory system tumours
1		Epithelial tumour of the trachea	C33
2		Variants of squamous cell carcinoma of the trachea	C33
3		Squamous carcinoma	C33
3		Papillary squamous cell carcinoma	C33
3		Basaloid squamous cell carcinoma	C33
3		Squamous cell carcinoma clear cell type	C33
3		Verrucous carcinoma	C33
3		Squamous cell carcinoma, adenoid	C33
3		Spindle cell carcinoma	C33
3		Adenosquamous carcinoma	C33
3		Lymphoepithelial carcinoma	C33
3		Giant cell carcinoma	C33
3		Undifferentiated carcinoma	C33
2		Variants of adenocarcinoma of the trachea	C33
3		Adenocarcinoma, NOS	C33
3		Mucinous adenocarcinoma	C33
3		Papillary adenocarcinoma, NOS	C33
3		Solid carcinoma, NOS	C33
3		Clear cell adenocarcinoma, NOS	C33
3		Acinar cell adenocarcinoma	C33
3		Signet ring cell carcinoma	C33
3		Mucinous cystadenocarcinoma, NOS	C33
2		Salivary-gland-type tumours of the trachea	C33
3		Adenoid cystic carcinoma	C33
3		Mucoepidermoid carcinoma	C33
3		Myoepithelial carcinoma	C33
2		Typical and atypical carcinoid of the lung	C34
3		Well-differentiated endocrine tumours, carcinoid	All cancer sites except C15-C26, C34, C44, C48, C51, C60, C63.2, C73
3		Well-differentiated endocrine tumours, atypical carcinoid	All cancer sites except C15-C26, C34, C44, C48, C51, C60, C63.2, C73
3		Poorly differentiated endocrine carcinoma	All cancer sites except C15-C26, C34, C44, C48, C51, C60, C63.2, C73
2		Salivary-gland-type tumours of the lung	C34
2		Sarcomatoid carcinoma of the lung	C34
2		NUT Carcinoma of the Lung	C34
1		Epithelial tumours of the thymus	C37
2		Malignant thymoma	C37
3		Thymoma, malignant, NOS	C37
3		Malignant thymoma, type AB	C37
3		Malignant thymoma, type A	C37
3		Malignant thymoma, type B	C37
3		Malignant thymoma, type C	C37
2		Squamous cell carcinoma of the thymus	C37
2		Undifferentiated carcinoma of the thymus	C37
2		Lymphoepithelial carcinoma of the thymus	C37
2		Variants of adenocarcinoma of the thymus	C37
3		Adenocarcinoma, NOS	C37
3		Papillary adenocarcinoma, NOS	C37
	4. Reproductive system tumours
3		Breast Invasive Carcinosarcoma, NOS	C50
3		Breast Carcinoma with Signet Ring	C50
3		Metaplastic Carcinosarcoma	C50
2		Salivary-gland-type tumours of the breast	C50
3		Mucoepidermoid carcinoma	C50
3		Adenoid cystic breast cancer	C50
3		Myoepithelial carcinoma	C50
3		Acinar cell adenocarcinoma	C50
1		Unspecified tumour of uteri	C55
2		Adenoid cystic carcinoma of corpus uteri	C54, C55
2		Clear cell adenocarcinoma, NOS	C54, C55
2		Small cell carcinoma ≠ NET	C54, C55
2		Gestational trophoblastic disease	C54, C55
1		Epithelial tumours of the ovary and fallopian tube	C57
2		Clear cell ovarian cancer	C56
2		Mullerian mixed tumour of the ovary	C56
2		Small cell ≠ NET	C56
2		Sex cord tumours of the ovary	C56
2		Malignant/Immature teratomas of the ovary	C56
2		Germ cell tumour of the ovary	C56
1		Eepithelial tumours of the vagina	C52
2		Squamous cell carcinoma of the vulva/vagina	C51
2		Variants of adenocarcinoma of the vulva and vagina	C51
2		Germ cell tumour of the vulva	C51
1		Eepithelial tumours of the vulva	C51
2		Paget’s disease of vulva and vagina	C51
2		Poorly differentiated vaginal carcinoma	C52
1		Trophoblastic tumour of the placenta	C58
2		Choriocarcinoma of the placenta	C58
1		Other and unspecified male reproductive organs	C63
3		Adenoid cystic carcinoma	C61
2		Prostate Small Cell Carcinoma	C61
1		Tsticular and paratesticular cancers	C62
2		Variants of paratesticular adenocarcinoma	C62,C63
2		Non-seminomatous testicular cancer	C62
2		Seminomatous testicular cancer	C62
2		Spermatocytic seminoma	C62
2		Teratoma with malignant transformation	C62
2		Testicular sex cord cancer	C62
2		Testicular mesothelioma	C62
1		Epithelial tumours of the penis	C60
2		Variants of squamous cell carcinoma of the penis	C60
2		Variants of adenocarcinoma of the penis	C60
1		Extragonadal germ cell tumours	All sites
2		Non-seminomatous germ cell tumours	All cancers sites except C56, C58 and C62
3		Embryonal adenocarcinoma, NOS	All cancer sites except C56, C58, C62, C71–C72, C75.1, C75.3
3		Yolk sac tumour	All cancer sites except C56, C58, C62, C71–C72, C75.1, C75.3
3		Teratocarcinoma	All cancer sites except C56, C58, C62, C71–C72, C75.1, C75.3
3		Teratoma with malignant transformation	All cancer sites except C56, C58, C62, C71–C72, C75.1, C75.3
3		Germ cell tumour with somatic-type malignancy	All cancer sites except C56, C58, C62, C71–C72, C75.1, C75.3
3		Mixed germ cell tumour	All cancer sites except C56, C58, C62, C71–C72, C75.1, C75.3
3		Choriocarcinoma, NOS	All cancer sites except C56, C58, C62, C71–C72, C75.1, C75.3
3		Choriocarcinoma combined with other germ cell elements	All cancer sites except C56, C58, C62, C71–C72, C75.1, C75.3
2		Seminomatous germ cell tumours	All cancer sites except C56, C58, C62, C71–C72, C75.1, C75.3
3		Dysgerminoma	All cancer sites except C56, C58, C62, C71–C72, C75.1, C75.3
3		Seminoma, NOS	All cancer sites except C56, C58, C62, C71–C72, C75.1, C75.3
3		Seminoma, anaplastic	All cancer sites except C56, C58, C62, C71–C72, C75.1, C75.3
3		Spermatocytic seminoma	All cancer sites except C56, C58, C62, C71–C72, C75.1, C75.3
2		Germ cell tumours of central nervous system (CNS)	C71–C72, C75.1, C75.3
3		Dysgerminoma	C71–C72, C75.1, C75.3
3		Seminoma, NOS	C71–C72, C75.1, C75.3
3		Seminoma, anaplastic	C71–C72, C75.1, C75.3
3		Spermatocytic seminoma	C71–C72, C75.1, C75.3
3		Embryonal adenocarcinoma, NOS	C71–C72, C75.1, C75.3
3		Yolk sac tumour	C71–C72, C75.1, C75.3
3		Teratocarcinoma	C71–C72, C75.1, C75.3
3		Teratoma with malignant transformation	C71–C72, C75.1, C75.3
3		Mixed germ cell tumour	C71–C72, C75.1, C75.3
3		Choriocarcinoma, NOS	C71–C72, C75.1, C75.3
3		Choriocarcinoma combined with other germ cell elements	C71–C72, C75.1, C75.3
	5. Urinary system tumours
3		Sarcomatoid renal cell carcinoma	C64
2		Rhabdoid cancer (MRT)	C64
2		Clear cell sarcoma of the kidney	C64
2		Variants of adenocarcinoma of the pelvis and ureter	C65, C66
1		Epithelial tumours of the urethra	C68
2		Transitional cell carcinoma of the urethra	C68
3		Undifferentiated carcinoma	C68
3		Transitional cell carcinoma, spindle cell	C68
3		Lymphoepithelioma-like carcinoma	C68
3		Transitional cell carcinoma, giant cell	C68
3		Transitional cell carcinoma, micropapillary	C68
2		Variants of squamous cell carcinoma of the urethra	C68
3		Basaloid carcinoma	C68
3		Verrucous carcinoma	C68
2		Variants of adenocarcinoma of the urethra	C68
3		Mucinous adenocarcinoma	C68
3		Clear cell adenocarcinoma, NOS	C68
3		Signet ring cell carcinoma	C68
3		Adenoid cystic carcinoma	C68
2		Urachal adenocarcinoma	C68
2		Salivary-gland-type tumours of the bladder	C67
3		Adenoid cystic carcinoma	C67
3		Mucoepidermoid carcinoma	C67
2		Sarcomatoid carcinoma of the urinary bladder	C67
2		Small cell bladder cancer	C67
2		Inflammatory myofibroblastic bladder tumour	C67
	6. Malignant tumours involving multiple systems
1		Malignant mesothelioma	All cancer sites
2		Pleural mesothelioma	C45
2		Mesothelioma of pleura and pericardium	C38
3		Epithelioid malignant mesothelioma	C38
3		Sarcomatoid malignant mesothelioma	C38
2		Mesothelioma of peritoneum and tunica vaginalis	C48, C63
3		Epithelioid malignant mesothelioma	C48, C63
3		Sarcomatoid malignant mesothelioma	C48, C63
2		Primary peritoneal serous/papillary carcinoma	C48
2		Neuroendocrine carcinoma of other sites	All cancer sites except C15–C26, C34, C44, C48, C51, C60, C63.2, C73
3		Well-differentiated endocrine tumours, carcinoid	All cancer sites except C15–C26, C34, C44, C48, C51, C60, C63.2, C73
3		Well-differentiated endocrine tumours, atypical carcinoid	All cancer sites except C15–C26, C34, C44, C48, C51, C60, C63.2, C73
3		Poorly differentiated endocrine carcinoma	All cancer sites except C15–C26, C34, C44, C48, C51, C60, C63.2, C73
1		Neuroblastoma and ganglioneuroblastoma	All cancers sites, except CNS and Autonomic Nervous System and peripheral nerves
2		Neuroblastoma and ganglioneuroblastoma	All cancers sites, except CNS and Autonomic Nervous System and peripheral nerves
1		Nephroblastoma	C64
2		Nephroblastoma	C64
1		Retinoblastoma	C69
2		Retinoblastoma	C69
1		Hepatoblastoma	C22
2		Hepatoblastoma	C22
1		Pleuropulmonary blastoma	C34
2		Pleuropulmonary blastoma	C34
1		PANCREATOBLASTOMA	C25
2		Pancreatoblastoma	C25
1		Olfactory neuroblastoma	C30,C31
2		Olfactory neuroblastoma	C30,C31
	7. Cutaneous malignant tumour
1		Epithelial tumours of the skin	C44
2		Neuroendocrine carcinoma of the skin	C44.0–C44.9, CC51.0–C51.9, C60.0,C60.9 C63.2
3		Merkel cell carcinoma	C44.0–C44.9, CC51.0–C51.9, C60.0,C60.9 C63.2
2		Basal cell carcinoma of the skin	C44
3		Basal cell carcinoma, NOS	C44
3		Basosquamous carcinoma	C44
3		Multifocal superficial basal cell carcinoma	C44
3		Basal cell carcinoma nodular	C44
3		Basal cell carcinoma fibroepithelial	C44
3		Adenoid basal carcinoma	C44
2		Variants of squamous cell carcinoma of the skin	C44
3		Squamous carcinoma	C44
3		Verrucous carcinoma	C44
3		Spindle cell carcinoma	C44
3		Pseudovascular/squamous cell carcinoma adenoid	C44
3		Adenosquamous carcinoma	C44
1		Adnexal carcinoma of the skin	C44
2		Adnexal carcinoma of the skin	C44
3		Nodular hidradenoma, malignant	C44
3		Sebaceous adenocarcinoma	C44
3		Adenoid cystic carcinoma	C44
3		Paget’s disease extramammary	C44
3		Apocrine adenocarcinoma	C44
3		Mucinous adenocarcinoma	C44
3		Pilomatrix carcinoma	C44
3		Eccrine poroma, malignant	C44
3		Mixed tumour malignant, NOS	C44
3		Sclerosing sweat duct carcinoma	C44
3		Malignant eccrine spiradenoma	C44
3		Tubular adenocarcinoma	C44
3		Eccrine papillary adenocarcinoma	C44
	8. Malignant tumour of soft tissue
1		Soft tissue sarcoma	C49
3		Aggressive angiomyxoma	All cancers sites except C40.0–C41.9
3		Alveolar soft part sarcoma	All cancers sites except C40.0–C41.9
3		Angiomatoid fibrous histiocytoma	All cancers sites except C40.0–C41.9
3		Angiosarcoma	All cancers sites except C40.0–C41.9
3		Clear cell sarcoma	All cancers sites except C40.0–C41.9
3		Dendritic cell sarcoma	All cancers sites except C40.0–C41.9
3		Desmoid/aggressive fibromatosis (DES)	All cancers sites except C40.0–C41.9
3		Desmoplastic small-round-cell tumour	All cancers sites except C40.0–C41.9
3		Epithelioid haemangioendothelioma	All cancers sites except C40.0–C41.9
3		Epithelioid sarcoma	All cancers sites except C40.0–C41.9
3		Fibrosarcoma	All cancers sites except C40.0–C41.9
3		Gastrointestinal stromal tumour	All cancers sites except C40.0–C41.9
3		Glomangiosarcoma	All cancers sites except C40.0–C41.9
3		Inflammatory Myofibroblastic Tumour	All cancers sites except C40.0–C41.9
3		Intimal Sarcoma	All cancers sites except C40.0–C41.9
3		Leiomyosarcoma	All cancers sites except C40.0–C41.9
3		Liposarcoma	All cancers sites except C40.0–C41.9
3		Dedifferentiated liposarcoma	All cancers sites except C40.0–C41.9
3		Myxoid/round-cell liposarcoma	All cancers sites except C40.0–C41.9
3		Pleomorphic liposarcoma	All cancers sites except C40.0–C41.9
3		Well-differentiated liposarcoma	All cancers sites except C40.0–C41.9
3		Low-grade fibromyxoid sarcoma	All cancers sites except C40.0–C41.9
3		Undifferentiated pleomorphic sarcoma/malignant fibrous histiocytoma/high-grade spindle cell sarcoma	All cancers sites except C40.0–C41.9
3		Myxofibrosarcoma	All cancers sites except C40.0–C41.9
3		Radiation-associated sarcoma	All cancers sites except C40.0–C41.9
3		Rhabdomyosarcoma	All cancers sites except C40.0–C41.9
3		Alveolar rhabdomyosarcoma	All cancers sites except C40.0–C41.9
3		Embryonal rhabdomyosarcoma	All cancers sites except C40.0–C41.9
3		Pleomorphic rhabdomyosarcoma	All cancers sites except C40.0–C41.9
3		Spindle cell rhabdomyosarcoma	All cancers sites except C40.0–C41.9
3		Spindle cell/sclerosing rhabdomyosarcoma	All cancers sites except C40.0–C41.9
3		Round cell sarcoma, NOS (RCSNOS)	All cancers sites except C40.0–C41.9
3		RCSNOS	All cancers sites except C40.0–C41.9
3		Sarcoma, NOS (SARCNOS)	All cancers sites except C40.0–C41.9
3		Solitary fibrous tumour/haemangiopericytoma	All cancers sites except C40.0–C41.9
3		Soft tissue myoepithelial carcinoma	All cancers sites except C40.0–C41.9
3		Synovial sarcoma	All cancers sites except C40.0–C41.9
3		Ewing sarcoma of soft tissue	All cancers sites except C40.0–C41.9
3		Infantile fibrosarcoma	All cancers sites except C40.0–C41.9
3		Malignant glomus tumour	All cancers sites except C40.0–C41.9
2		Soft tissue sarcoma of the head and neck	C00.0–C14.8, C30.0–C32.9, C49.0, C73.9, C75.2, C75.4, C76.0
2		Soft tissue sarcoma of the limbs*	C49.1–C49.2, C76.4–C76.5
2		Soft tissue sarcoma of the superficial trunk*	C49.3–C49.4, C49.6, C76.1–C76.2, C76.7
2		Soft tissue sarcoma of the mediastinum*	C38.1–C38.3, C38.8
2		Soft tissue sarcoma of the heart*	C38.0
2		Soft tissue sarcoma of the breast*	C50.0–C50.9
2		Soft tissue sarcoma of the uterus*	C53.0–C55.9
3		Undifferentiated Uterine Sarcoma	C53.0–C55.9
3		Uterine Adenosarcoma	C53.0–C55.9
3		Endometrial stromal sarcoma (ESS)	C53.0–C55.9
3		High-grade ESS (HGESS)	C53.0–C55.9
3		Low-grade ESS	C53.0–C55.9
3		Uterine smooth muscle tumour	C53.0–C55.9
3		Uterine leiomyosarcoma	C53.0–C55.9
3		Uterine epithelioid leiomyosarcoma	C53.0–C55.9
3		Uterine myxoid leiomyosarcoma	C53.0–C55.9
2		Soft tissue sarcoma of the paratestis*	C63.0–C63.7
2		Soft tissue sarcomas of other genitourinary tract structures (vulva, vagina, ovary, penis, prostate, testis, kidney, renal pelvis, ureter, bladder, urethra)	C51.0–C52.9, C56.9–C57.9, C60.0–C62.9, C63.8–C63.9, C64.9–C68.9
3		Clear cell sarcoma of the kidney	64.9
3		Malignant rhabdoid tumour of the kidney	64.9
2		Soft tissue sarcoma of the viscera*	C15.0–C26.9, C33.9–C37.9, C38.4, C39.0–C39.9, C42.2
2		Soft tissue sarcoma of retroperitoneum and peritoneum*	C48.0–C48.8
2		Soft tissue sarcoma of the pelvis*	C49.5, C76.3
2		Soft tissue sarcoma of the skin*	C44.0–C44.9
2		Soft tissue sarcoma of the paraorbit*	C69.0–C69.9
2		Soft tissue sarcoma of brain and other parts of the nervous system*	C47.0–C47.9, C70.0–C72.9, C75.1, C75.3
2		Embryonal rhabdomyosarcoma of soft tissue	All cancers sites except C40.0–C41.9
2		Alveolar rhabdomyosarcoma of soft tissue	All cancers sites except C40.0–C41.9, C56 and C62
2		Ewing’s sarcoma of soft tissue	All cancers sites except C40.0–C41.9, C56 and C62, C71, C72
3		Ewing sarcoma	All cancers sites except C40.0–C41.9, C56 and C62, C71, C72
3		Peripheral neuroectodermal tumour	All cancers sites except C40.0–C41.9, C56 and C62, C71, C72
3		Primitive neuroectodermal tumour, NOS	All cancers sites except C40.0–C41.9, C56 and C62, C71, C72
	9. Malignant tumour of bone and joint system
1		Bone sarcoma	C40
1		Bone sarcoma	C41
2		Osteogenic sarcoma	C40–41
3		Conventional osteosarcoma	C40–41
3		Telangiectatic osteosarcoma	C40–41
3		Small cell osteosarcoma	C40–41
3		Paraosteal osteosarcoma	C40–41
3		High-grade surface osteosarcoma	C40–41
3		Low-grade central osteosarcoma	C40–41
3		Periosteal osteosarcoma	C40–41
3		Secondary osteosarcoma	C40–41
2		Chondrogenic sarcomas	C40–41
3		Chondrosarcoma	C40–41
3		Mesenchymal chondrosarcoma	C40–41
3		Clear cell chondrosarcoma	C40–41
3		Dedifferentiated chondrosarcoma	C40–41
2		Notochordal sarcomas, chordoma	C40–41
2		Vascular sarcomas	C40–41
3		Angiosarcoma	C40–41
2		Ewing’s sarcoma	C40–41
3		Peripheral neuroectodermal tumour	C40–41
2		Epithelial tumours, adamantinoma	C40–41
2		Other high-grade sarcomas (fibrosarcoma, malignant fibrous histiocytoma)	C40–41
3		Fibrosarcoma	C40–41
3		Malignant fibrous histiocytoma	C40–41
	10. Malignant tumours of endocrine system
1		Carcinomas of the parathyroid gland	C75
2		Carcinomas of the pituitary gland	C75
3		Pituitary carcinoma	C75
1		Carcinomas of the parathyroid gland	C75
2		Carcinomas of the parathyroid gland	C75
1		Carcinoma of the adrenal cortex	C74
2		Carcinoma of adrenal cortex	C74
3		Adrenal cortical carcinoma	C74
	11. Malignant tumour of nervous system
1		Malignant tumour of cerebrospinal membrane	C70
1		Malignant tumours of the spinal cord, cranial nerves and other parts of the CNS	C72
2		Astrocytic tumours of the CNS	C71, C72
3		Astrocytoma, NOS	C71, C72
3		Astrocytoma, anaplastic	C71, C72
3		Glioblastoma	C71,
3		Gliosarcoma	C71, C72
3		Giant cell glioblastoma	C71, C72
3		Astroblastoma	C71, C72
3		Protoplasmic astrocytoma	C71, C72
3		Gliomatosis cerebri	C71, C72
3		Pleomorphic xanthoastrocytoma	C71, C72
3		Pilocytic and Pilomyxoid astrocytoma	C71, C72
3		Oligoastrocytoma	C71, C72
3		Anaplastic Oligoastrocytoma	C71, C72
3		Subependymal giant cell astrocytoma	C71, C72
2		Oligodendroglial tumours of the CNS	C71, C72
3		Oligodendroglioma	C71, C72
3		Oligodendroglioma, anaplastic	C71, C72
3		Anaplastic Oligodendroglioma	C71, C72
2		Ependymal tumours of the CNS	C71, C72
3		Ependymoma, NOS	C71, C72
3		Ependymoma, anaplastic	C71, C72
3		Clear Cell Ependymoma	C71, C72
3		Subependymoma	C71, C72
3		Myxopapillary ependymoma	C71, C72
2		Neuronal and mixed neuronal-glial tumours	C71, C72
2		Choroid plexus carcinoma of the CNS	C71
2		Malignant meningiomas	C70
3		Meningioma	C70
3		Anaplastic meningioma	C70
3		Atypical meningioma	C70
3		Chordoid meningioma	C70
3		Clear cell meningioma	C70
3		Haemangiopericytoma of the CNS	C70
3		Papillary Meningioma	C70
3		Rhabdoid Meningioma	C70
1		Embryonal tumours of the CNS	C71, C72, C75.3
2		Embryonal tumours of the CNS	C71, C72, C75.3
3		Medulloblastoma	C71, C72
3		Desmoplastic nodular medulloblastoma	C71, C72
3		CNS-PNET	C71, C72
3		Atypical teratoid/rhabdoid tumour	C71, C72
3		Medulloepithelioma, NOS	C71, C72
3		Pineoblastoma	C75.3
3		Ependymoblastoma	C71, C72
3		Neuroepithelioma, NOS	C71, C72
3		Atypical teratoid/rhabdoid tumour	C71, C72
3		Desmoplastic/nodular medulloblastoma	C71, C72
3		Embryonal tumour with abundant neuropil and true rosettes	C71, C72
3		Ganglioneuroblastoma	C71, C72
3		Large cell/anaplastic medulloblastoma	C71, C72
3		Medulloblastoma with extensive nodularity	C71, C72
3		Medullomyoblastoma	C71, C72
3		Melanotic medulloblastoma	C71, C72
3		Neuroblastoma	C71, C72
1	12. Cancer of unknown primary origin
1		Cancer of unknown primary origin of other and unspecified sites	C76
1		Cancer of unknown primary origin of the lymph nodes	C77
1		Malignant tumour of unspecified sites	C80
2		Cancer of unknown primary origin in the digestive system	C26
2		Cancer of unknown primary origin in the respiratory and thoracic cavity	C39
3		Acinar cell carcinoma, NOS	C39, C26, C76, C77, C80
3		Adenocarcinoma, NOS	C39, C26, C76, C77, C80
3		Cancer of unknown primary origin, NOS	C39, C26, C76, C77, C80
3		Mixed cancer types (MIXED)	C39, C26, C76, C77, C80
3		Neuroendocrine carcinoma, NOS	C39, C26, C76, C77, C80
3		Neuroendocrine tumour, NOS	C39, C26, C76, C77, C80
3		Poorly differentiated carcinoma, NOS	C39, C26, C76, C77, C80
3		Small cell carcinoma of unknown primary origin	C39, C26, C76, C77, C80
3		Squamous cell carcinoma, NOS	C39, C26, C76, C77, C80
3		Undifferentiated malignant neoplasm	C39, C26, C76, C77, C80

*Head and neck, limbs, superficial trunk, mediastinum, heart, breast, uterus, paratestis, viscera, retroperitoneum and peritoneum, skin, paraorbit, brain and other parts of the nervous system.
DES, desmoid tumors; IBT, intrahepatic biliary tract; ICD, International Classification of Diseases; MRT, Malignant rhabdoid-tumor; NOS, not otherwise specified; PNET, primitive neurotodermal tumour.