Read code descriptions (based on pre-1997 nomenclature) | EDS type according to the Villefranche criteria | EDS type according to the March 2017 criteria | Read code version 2 | ICD-10 code |
Ehlers-Danlos syndrome | PGy2. | Q79.6 | ||
Ehlers-Danlos syndrome type I | Classical type | Classical EDS | PGy20 | |
Ehlers-Danlos syndrome type II | PGy21 | |||
Ehlers-Danlos syndrome type III | Hypermobility type | Hypermobile EDS or hypermobility spectrum disorder | PGy22 | |
Ehlers-Danlos syndrome type IV | Vascular type | Vascular EDS | PGy23 | |
Ehlers-Danlos syndrome type V | X-linked type | No longer classified as EDS | PGy24 | |
Ehlers-Danlos syndrome type VI | Kyphoscoliotic type | Kyphoscoliotic EDS | PGy25 | |
Ehlers-Danlos syndrome type VII | Arthrochalasia type Dermatosparaxis type | Arthrochalasia EDS Dermatosparaxis EDS | PGy26 | |
Ehlers-Danlos syndrome type VIII | Periodontitis type | Periodontal EDS | PGy27 | |
Hypermobility syndrome (JHS according to the Brighton Criteria) | Hypermobility type | Hypermobile EDS or hypermobility spectrum disorder | N235. | 728.5 |
EDS, Ehlers-Danlos syndrome; ICD-10, International Statistical Classification of Diseases and Related Health Problems, 10th Revision; JHS, joint hypermobility syndrome.