Age at onset in familial index cases and their relatives carrying 1–3 DRA
| (A) | ||||
|---|---|---|---|---|
| Mean age at onset | ||||
| 1–3 DRA carriers | Number of participants | Years | SD | p Value* |
| Probands | 26 | 13.1 | 10.1 | |
| Relatives | 29 | 17.1 | 14.2 | 0.019 |
| Total | 55 | |||
| (B) | |||||||
|---|---|---|---|---|---|---|---|
| Age at onset | |||||||
| 0–10 years | >10 years | Unaffected | |||||
| 1–3 DRA index cases | Number of participants | Number of participants | Per cent | Number of participants | Per cent | Number of participants | Per cent |
| Probands | 26 | 12 | 38.5 | 14 | 61.5 | 0 | 0.0 |
| Relatives | 33 | 13 | 39.4 | 16 | 48.5 | 4 | 12.1 |
*Wilcoxon rank-sum test p value.