Clinical manifestations of plaque-type cases
| Total (n=18)* | Supratentorial group (n=9) | Infratentorial group (n=8) | p Value† | |
|---|---|---|---|---|
| Pathologically confirmed cases (%) | 14 (78) | 7 (78) | 6 (75) | ns |
| Initial manifestations‡ (%) | (n=14) | (n=8) | (n=5) | |
| Unsteady gait | 9 (64) | 6 (75) | 2 (40) | ns |
| Dementia | 2 (14) | 1 (13) | 1 (20) | ns |
| Vertigo | 3 (21) | 1 (13) | 2 (40) | ns |
| Diplopia | 1 (7) | 0 (0) | 0 (0) | ns |
| Sensory disturbance | 1 (7) | 0 (0) | 1 (20) | ns |
| Others§ | 2 (14) | 2 (25) | 0 (0) | — |
| Manifestations during clinical course (%) | ||||
| Cerebellar signs | 16/18 (89) | 8/9 (89) | 7/8 (88) | ns |
| Psychiatric feature | 10/16 (63) | 4/8 (50) | 5/7 (71) | ns |
| Dementia | 18/18 (100) | 9/9 (100) | 8/8 (100) | ns |
| Visual disturbance | 11/18 (61) | 5/9 (56) | 5/8 (63) | ns |
| Myoclonus | 14/18 (78) | 8/9 (89) | 6/8 (75) | ns |
| Extrapyramidal signs | 14/18 (78) | 8/9 (89) | 6/8 (75) | ns |
| Pyramidal signs | 8/17 (47) | 5/8 (63) | 3/8 (38) | ns |
*Total includes one case with an uncertain grafting region.
†p Value was assessed between the supratentorial group and the infratentorial group; ns, not significant.
‡Four cases of the total, two cases of the supratentorial group and one case of the infratentorial group developed more than one initial manifestation.
§Others include individual cases of incontinence and hearing disturbance.